Fall 2004; 47(85):337-342.

A CASE REPORT OF BOTRYOID SARCOMA OF BILIARY TRACT

BADIEE Z., ZABOLYNEJAD N., BAZRQFSHAN A.

Rhabdomyosarcoma of biliary tract system (RMS/BT) is a very rare form of RMS that usually presents with jaundice in young children. In some rane cases icter disappears transiently and causes delay in diagnosis, there fore this condition must be included in differential diagnosis of obstructive jaundice in infants and children.

Ultrasonography is very useful for diagnosis of abdominal mass and clarifying its relationship with the biliary tract system. Surgery is critical for estabilishing accurate diagnosis and determining the extent of regional disease, but aggressive surgery is not recommended because, despite gross residual mass after surgery the outcome of chemotherapy +/- radiotherapy is sufficient. Because this tumor is very rare and its treatment has improved in recent years we report a case of RMS/BT in a I5-month girl who presented with abdominal mass and history of obstructivejaundice

Keyword: Botryoide Sarcoma, Embryonal Rhabdomyosarcoma, Biliary tract